Dental considerations and management in Noonan Syndrome: A case report with review of literature

Case Report

Contemp Pediatr Dent 2021:2(2):126-133


Dental considerations and management in Noonan Syndrome: A case report with review of literature

OrcidNipun Jain1, OrcidPriyanka Venugopal2 OrcidArun Mamachan Xavier3 ✉, OrcidParvathy Kumaran4 OrcidBalagopal R Varma5, OrcidSuresh Kumar J6

Affiliations

1. Post Graduate Student, Department of Pediatric and Preventive Dentistry, Amrita School of Dentistry, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

2. Post Graduate Student, Department of Pediatric and Preventive Dentistry, Amrita School of Dentistry, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

3. Reader, Department of Pediatric and Preventive Dentistry, Amrita School of Dentistry, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India ( Correspondence: arunmamachan@yahoo.co.in)

4. Professor, Department of Pediatric and Preventive Dentistry, Amrita School of Dentistry, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

5. Professor, Department of Pediatric and Preventive Dentistry, Amrita School of Dentistry, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

6.Professor, Department of Pediatric and Preventive Dentistry, Amrita School of Dentistry, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India


Highlights

Noonan syndrome is a relatively common genetic disorder seen in dental practise.

Not all dental characteristic features are seen at a given time.

Children with Noonan syndrome are generally uncooperative in dental chair and owing to their systemic complications; dental management is mostly carried out under general anaesthesia.


Abstract

Noonan syndrome is a genetic disorder of autosomal dominance with an estimated prevalence of 1:1000 – 1:2500 live birth. The typical features include short stature, cardiovascular abnormalities and characteristics facial deformity. Dental features reported so far include malocclusion, dental caries, giant cell and cystic lesion. Multidisciplinary treatment plays a key role in the overall quality of life of the patient. This case report describes a 6-year-old boy with Noonan syndrome.

Keywords: Cardiovascular Abnormalities; Comprehensive Dental Care; Noonan Syndrome


Copyright © 2021 Contemporary Pediatric Dentistry

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Full Text


DOI

10.51463/cpd.2021.57


Views

198 views

Article Info

Received:

13 May 2021

Accepted:

15 June 2021

Online First:

23 June 2021