Dental considerations and management in Noonan Syndrome: A case report with review of literature

Nipun Jain1Orcid, Priyanka Venugopal2Orcid, Arun Mamachan Xavier3Orcid, Parvathy Kumaran4Orcid, Balagopal R Varma5Orcid, Suresh Kumar J6Orcid

Highlights

Noonan syndrome is a relatively common genetic disorder seen in dental practise.
Not all dental characteristic features are seen at a given time.
Children with Noonan syndrome are generally uncooperative in dental chair and owing to their systemic complications; dental management is mostly carried out under general anaesthesia.

Abstract

Noonan syndrome is a genetic disorder of autosomal dominance with an estimated prevalence of 1:1000 – 1:2500 live birth. The typical features include short stature, cardiovascular abnormalities and characteristics facial deformity. Dental features reported so far include malocclusion, dental caries, giant cell and cystic lesion. Multidisciplinary treatment plays a key role in the overall quality of life of the patient. This case report describes a 6-year-old boy with Noonan syndrome.

Keywords: Cardiovascular Abnormalities; Comprehensive Dental Care; Noonan Syndrome

Author Affiliations

  1. Post Graduate Student, Department of Pediatric and Preventive Dentistry, Amrita School of Dentistry, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India
  2. Post Graduate Student, Department of Pediatric and Preventive Dentistry, Amrita School of Dentistry, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India
  3. Reader, Department of Pediatric and Preventive Dentistry, Amrita School of Dentistry, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India (✉ Correspondence: arunmamachan@yahoo.co.in)
  4. Professor, Department of Pediatric and Preventive Dentistry, Amrita School of Dentistry, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India
  5. Professor, Department of Pediatric and Preventive Dentistry, Amrita School of Dentistry, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India
  6. Professor, Department of Pediatric and Preventive Dentistry, Amrita School of Dentistry, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India
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Article Info

Contemp Pediatr Dent 2021:2(2):126-133

Received: 13 May 2021

Accepted: 15 June 2021

Online First: 23 June 2021

DOI: 10.51463/cpd.2021.57

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					Nipun Jain, Priyanka Venugopal, Arun Mamachan Xavier, Parvathy Kumaran, Balagopal R Varma, Suresh Kumar J. Dental considerations and management in Noonan Syndrome: A case report with review of literature. Contemp Pediatr Dent 2021:2(2):126-133.

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